Endoplasmic reticulum Ca2+ increases enhance mutant glucocerebrosidase proteostasis
Journal Article
Overview
publication date
- June 1, 2010
has subject area
- Adenosine Triphosphatases - Sarcoplasmic Reticulum Calcium-Transporting ATPases
- Biochemical Phenomena - Protein Folding
- Biochemical Phenomena - Protein Processing, Post-Translational
- Biochemical Phenomena - Protein Processing, Post-Translational
- Biological Factors - Calcium
- Biophysical Phenomena - Protein Folding
- Brain Diseases - Gaucher Disease
- Cardiovascular Agents - Calcium Channel Blockers
- Carrier Proteins - Ryanodine Receptor Calcium Release Channel
- Carrier Proteins - Sarcoplasmic Reticulum Calcium-Transporting ATPases
- Diltiazem
- Elements - Calcium
- Endoplasmic Reticulum
- Gene Expression Regulation - Protein Processing, Post-Translational
- Genetic Diseases, Inborn - Gaucher Disease
- Genetic Diseases, Inborn - Gaucher Disease
- Genetic Diseases, Inborn - Gaucher Disease
- Glucosylceramidase
- Humans
- Lipid Metabolism Disorders - Gaucher Disease
- Lysosomes
- Membrane Proteins - Ryanodine Receptor Calcium Release Channel
- Membrane Proteins - Ryanodine Receptor Calcium Release Channel
- Membrane Proteins - Sarcoplasmic Reticulum Calcium-Transporting ATPases
- Membrane Transport Modulators - Calcium Channel Blockers
- Metabolic Diseases - Gaucher Disease
- Metabolic Diseases - Gaucher Disease
- Metabolic Diseases - Gaucher Disease
- Metabolic Diseases - Gaucher Disease
- Metabolism - Protein Processing, Post-Translational
- Metals - Calcium
- Muscle Proteins - Ryanodine Receptor Calcium Release Channel
- Mutagenesis - Amino Acid Substitution
- Protein Engineering - Amino Acid Substitution
- Vasodilator Agents
- Verapamil
Full Author List
- Ong DST; Mu T-W; Palmer AE; Kelly JW
published in
- Nature Chemical Biology Journal
Other Profiles
Digital Object Identifier (DOI)
Additional Document Info
start page
- 424
end page
- 432
volume
- 6
issue
- 6